Hyperimmunoglobulin E syndrome
نویسندگان
چکیده
The article presents a clinical case of rare primary immunodeficiency syndrome Hyperimmunoglobulinemia E. Typical symptoms, diagnostic and treatment tactics have been demonstrated.
منابع مشابه
Hyperimmunoglobulin E syndrome.
Hyperimmunoglobulin E (HIE) syndrome is a primary immunodeficiency disorder characterized by recurrent bacterial infections in presence of very high serum Ig E levels. We are reporting a nine-year-old child with HIE syndrome and reviewing literature on this disease.
متن کاملThe hyperimmunoglobulin E syndrome.
Hyperimmunoglobulin E syndrome is a primary immunodeficiency disease characterized by markedly high titers of serum immunoglobulin E (IgE), chronic eczema, recurrent staphylococcal infections, pneumatoceles, reduced neutrophil chemotaxis, and variable impaired T cell function. There are no clinical tools for diagnosis and definitive laboratory investigation. Variability of presentation makes it...
متن کاملHyperimmunoglobulin E syndrome associated with nephrotic syndrome.
A 21-year-old man was admitted to Kure National Hospital with nephrotic syndrome in September 1996. He had suffered from an intractable pruritic skin rash and recurrent subcutaneous abscesses caused by the hyperimmunoglobulin E syndrome since the age of 18 months. Renal biopsy gave a diagnosis of membranoproliferative glomerulonephritis. Steroid therapy decreased urinary protein loss and hypopr...
متن کاملHyperimmunoglobulin E syndrome in two siblings
Hyperimmunoglobulin E recurrent infection syndrome (HIES) is characterized by recurrent skin and lung infections, eczema, elevated serum immunoglobulin E (IgE) levels (>2000 IU/mL), various connective tissue, skeletal, and vascular abnormalities.(1) We describe herein two brothers with HIES and documented the complications and management of such involvement.
متن کاملDescending necrotizing mediastinitis complicating hyperimmunoglobulin E syndrome
Descending necrotizing mediastinitis (DNM) is a potentially lethal disease that originates from a deep neck infection (DNI); it is often associated with an immunocompromised state. Hyperimmunoglobulin E syndrome (HIES) is an extremely rare complex immune deficiency characterized by recurrent abscesses of staphylococcal etiology. A rare case of a 34-year-old woman wherein HIES putatively promote...
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ژورنال
عنوان ژورنال: Problemy zdorov?â i èkologii
سال: 2023
ISSN: ['2708-6011', '2220-0967']
DOI: https://doi.org/10.51523/2708-6011.2023-20-1-17